Stomatologic management of dental malocclusion in patients with dystrophic epidermolysis bullosa using an interceptive guide of occlusion (IGO): Comparison of two cases

Abstract

Epidermolysis bullosa is a genetic syndrome that consists in the formation of blisters on the skin and oral epithelium in response to mechanical trauma. Epidermolysis bullosa is classifi ed into three major categories, including epidermolysis bullosa simplex, junctional epidermolysis bullosa, and dystrophic epidermolysis bullosa. The dental treatment of patients with epidermolysis bullosa represents a challenge due to the difficulty of operative techniques and the risk of causing blisters in the oral mucosa and also because of the microstomia that results from the cicatrization of injuries in oral epithelium. The pediatric dentist should treat the patient with an integral approach not only by means of restauration or mutilatory treatments, but including an individual risk analysis and prediction for the long term to guide the patient to an excellent status of oral health.Key words: Epidermolysis bullosa, serial extraction, microstomia, stomatologic management, guide of occlusion.